Se connecter

Bibliographies thématiques / Long-chain-acyl-CoA dehydrogenase

Sommaire

Articles de revues

Littérature scientifique sur le sujet « Long-chain-acyl-CoA dehydrogenase »

Auteur : Grafiati

Publié le 20 avril 2024

Créez une référence correcte selon les styles APA, MLA, Chicago, Harvard et plusieurs autres

Choisissez une source :

Consultez les listes thématiques d’articles de revues, de livres, de thèses, de rapports de conférences et d’autres sources académiques sur le sujet « Long-chain-acyl-CoA dehydrogenase ».

À côté de chaque source dans la liste de références il y a un bouton « Ajouter à la bibliographie ». Cliquez sur ce bouton, et nous générerons automatiquement la référence bibliographique pour la source choisie selon votre style de citation préféré : APA, MLA, Harvard, Vancouver, Chicago, etc.

Vous pouvez aussi télécharger le texte intégral de la publication scolaire au format pdf et consulter son résumé en ligne lorsque ces informations sont inclues dans les métadonnées.

Articles de revues sur le sujet "Long-chain-acyl-CoA dehydrogenase"

1

Masterson, C., A. Blackburn, and C. Wood. "Acyl-CoA dehydrogenase activity in pea cotyledon tissue during germination and initial growth." Biochemical Society Transactions 28, no. 6 (2000): 760–62. http://dx.doi.org/10.1042/bst0280760.

Texte intégral

Résumé :

Acyl-CoA dehydrogenase activity has been measured in homogenates of post-imbibition to 14-day-old hydroponically grown pea seeds at daily intervals, using C4, C12 and C16 acyl-CoA substrates. The activity peaks of the different chain-length acyl-CoA dehydrogenases did not transpose at all points and the ratios of the chain-length activities were not constant. It therefore has to be concluded that more than one dehydrogenase is present in pea mitochondria. There was a post-imbibition initial surge of activity with short- and mid-chain-length substrates. The C16- handling enzyme first peaked at

Styles APA, Harvard, Vancouver, ISO, etc.

2

Treem, William R., Jeffrey S. Hyams, Charles A. Stanley, Daniel E. Hale, and Harris B. Leopold. "Hypoglycemia, Hypotonia, and Cardiomyopathy: The Evolving Clinical Picture of Long-Chain Acyl-CoA Dehydrogenase Deficiency." Pediatrics 87, no. 3 (1991): 328–33. http://dx.doi.org/10.1542/peds.87.3.328.

Texte intégral

Résumé :

Inherited defects in fatty acid oxidation, which have been described and diagnosed with increasing frequency in the last decade, are most commonly attributed to a deficiency in the activity of medium-chain acyl-CoA dehydrogenase. Few cases of the related enzyme defect of long-chain acyl-CoA dehydrogenase activity have been reported. An infant with documented long-chain acyl-CoA dehydrogenase deficiency is described with a detailed metabolic profile, long-term clinical follow-up, and response to treatment. This patient is compared with the seven previously published cases of this disorder in or

Styles APA, Harvard, Vancouver, ISO, etc.

3

Cox, Keith B., Jian Liu, Liqun Tian, Stephen Barnes, Qinglin Yang, and Philip A. Wood. "Cardiac hypertrophy in mice with long-chain acyl-CoA dehydrogenase or very long-chain acyl-CoA dehydrogenase deficiency." Laboratory Investigation 89, no. 12 (2009): 1348–54. http://dx.doi.org/10.1038/labinvest.2009.86.

Texte intégral

Styles APA, Harvard, Vancouver, ISO, etc.

4

Yu, Wenfeng, Xiquan Liang, Regina E. Ensenauer, Jerry Vockley, Lawrence Sweetman та Horst Schulz. "Leaky β-Oxidation of atrans-Fatty Acid". Journal of Biological Chemistry 279, № 50 (2004): 52160–67. http://dx.doi.org/10.1074/jbc.m409640200.

Texte intégral

Résumé :

The degradation of elaidic acid (9-trans-octadecenoic acid), oleic acid, and stearic acid by rat mitochondria was studied to determine whether the presence of atransdouble bond in place of acisdouble bond or no double bond affects β-oxidation. Rat mitochondria from liver or heart effectively degraded the coenzyme A derivatives of all three fatty acids. However, with elaidoyl-CoA as a substrate, a major metabolite accumulated in the mitochondrial matrix. This metabolite was isolated and identified as 5-trans-tetradecenoyl-CoA. In contrast, little or none of the corresponding metabolites were de

Styles APA, Harvard, Vancouver, ISO, etc.

5

Wijayabandara, Maheshi, Champika Gamakaranage, and Dineshani Hettiarachchi. "Very-Long-Chain Acyl-Co-Enzyme A Dehydrogenase Deficiency Presenting as Rhabdomyolysis: First Case Report from Sri Lanka." Case Reports in Genetics 2020 (October 13, 2020): 1–5. http://dx.doi.org/10.1155/2020/8894518.

Texte intégral

Résumé :

Background. Rhabdomyolysis can be either inherited or acquired such as in metabolic myopathies. Very-long-chain acyl-CoA dehydrogenase deficiency is a rare fatty acid oxidation disorder which presents with different phenotypes, and the mild adult form can present as intermittent rhabdomyolysis. Here, we present the first adult case of very-long-chain acyl-CoA dehydrogenase deficiency presenting as rhabdomyolysis in a Sri Lankan patient. Case Presentation. A 36-year-old Sri Lankan man who was born to consanguineous parents presented with severe generalized muscle pain, stiffness, and dark-colou

Styles APA, Harvard, Vancouver, ISO, etc.

6

Liang, X., W. Le, D. Zhang, and H. Schulz. "Impact of the intramitochondrial enzyme organization on fatty acid oxidation." Biochemical Society Transactions 29, no. 2 (2001): 279–82. http://dx.doi.org/10.1042/bst0290279.

Texte intégral

Résumé :

The enzymes of mitochondrial β-oxidation are thought to be organized in at least two functional complexes, a membrane-bound, long-chain-specific β-oxidation system and a matrix system consisting of soluble enzymes with preferences for medium-chain and short-chain substrates. This hypothesis is supported by the observation that the inactivation of long-chain 3-ketoacyl-CoA thiolase by 4-bromotiglic acid (4-bromo-2-methylbut-2-enoic acid) causes the complete inhibition of palmitate β-oxidation even though 3-ketoacyl-CoA thiolase, which acts on 3-ketopalmitoyl-CoA, remains partly active. The obse

Styles APA, Harvard, Vancouver, ISO, etc.

7

Yamaguchi, Seiji, Yasuhiro Indo, Paul M. Coates, Takashi Hashimoto, and Kay Tanaka. "Identification of Very-Long-Chain Acyl-CoA Dehydrogenase Deficiency in Three Patients Previously Diagnosed with Long-Chain Acyl-CoA Dehydrogenase Deficiency." Pediatric Research 34, no. 1 (1993): 111–13. http://dx.doi.org/10.1203/00006450-199307000-00025.

Texte intégral

Styles APA, Harvard, Vancouver, ISO, etc.

8

Costa, Catarina G., Lambertus Dorland, Ulbe Holwerda та ін. "Simultaneous analysis of plasma free fatty acids and their 3-hydroxy analogs in fatty acid β-oxidation disorders". Clinical Chemistry 44, № 3 (1998): 463–71. http://dx.doi.org/10.1093/clinchem/44.3.463.

Texte intégral

Résumé :

Abstract We present a new derivatization procedure for the simultaneous gas chromatographic–mass spectrometric analysis of free fatty acids and 3-hydroxyfatty acids in plasma. Derivatization of target compounds involved trifluoroacetylation of hydroxyl groups and tert-butyldimethylsilylation of the carboxyl groups. This new derivatization procedure had the advantage of allowing the complete baseline separation of free fatty acids and 3-hydroxyfatty acids while the superior gas chromatographic and mass spectrometric properties of tert-butyldimethylsilyl derivatives remained unchanged, permittin

Styles APA, Harvard, Vancouver, ISO, etc.

9

Nandy, Andreas, Volker Kieweg, Franz-Georg Kräutle, et al. "Medium-Long-Chain Chimeric Human Acyl-CoA Dehydrogenase: Medium-Chain Enzyme with the Active Center Base Arrangement of Long-Chain Acyl-CoA Dehydrogenase†." Biochemistry 35, no. 38 (1996): 12402–11. http://dx.doi.org/10.1021/bi960785e.

Texte intégral

Styles APA, Harvard, Vancouver, ISO, etc.

10

Parsons, H. G., and V. C. Dias. "Intramitochondrial fatty acid metabolism: riboflavin deficiency and energy production." Biochemistry and Cell Biology 69, no. 7 (1991): 490–97. http://dx.doi.org/10.1139/o91-073.

Texte intégral

Résumé :

Inborn errors of fatty acid β-oxidation have contributed significantly to our understanding of intracellular fatty acid metabolism. The first intramitochondrial step in β-oxidation of fatty acyl-CoA of different chain lengths is catalyzed by the three chain length specific acyl-CoA dehydrogenases. Inherited deficiency of these enzymes has been reported. Some are riboflavin responsive. The first step of fatty acid oxidation is reviewed with specific emphasis on β-oxidation in newborn infants, rendered riboflavin deficient by phototherapy. Given that medium chain fatty acids are not stored as tr

Styles APA, Harvard, Vancouver, ISO, etc.

Plus de sources

Nous offrons des réductions sur tous les plans premium pour les auteurs dont les œuvres sont incluses dans des sélections littéraires thématiques. Contactez-nous pour obtenir un code promo unique!